One striking characteristic of Monomelic Amyotrophy is its tendency to affect young males predominantly. Although the exact reason for this male preponderance remains unclear, it has been a consistent observation in many reported cases. This unique demographic distribution has sparked investigations into potential genetic and hormonal factors that may contribute to the development of MMA. Another distinctive feature of MMA is the asymmetrical distribution of muscle weakness and wasting, with upper limb involvement being more common than the lower limbs. Patients often report weakness and wasting in one arm, typically the dominant limb, while the other arm remains relatively unaffected. This pattern of asymmetric weakness poses diagnostic challenges and can sometimes lead to misdiagnosis, especially in the early stages [1].