Institut deCancérologie du Gard,
France
Case Report
About the Rare Case of a Pelvic Primitive Neuro-ectodermal Tumor in a 37 Year Old Patient
Author(s): Florence Lai TiongFlorence Lai Tiong
Introduction: Primitive Neuro-Ectodermal Tumors (PNETs) belong to the group of malignant bone tumors. Their frequency is about 1% of sarcoma. The principal distinctive feature in a translocation concerning the EWS gene or t(11; 22)(q24; q12). They are even rarer when located in the extra-skeletal pelvic region. Case report: We report a case of a 37 year old female patient with a PNET in the pelvic region that is found after a spontaneous abortion. The tumor is localized on the right latero-uterine ligament. The tumoral size is of 10 cm. After the coelioscopic diagnosis, the patient was treated with neo-adjuvant chemotherapy according to VIDE protocol and ensuring an important diminishing of the size of the tumor. She then had a total radical hysterectomy associated with a lymph node resection. The diagnosis was confirmed by histology, immunohistology examinations and molecular biology.. Read More»
DOI:
10.4172/2165-7920.1000664
Journal of Clinical Case Reports received 1345 citations as per Google Scholar report