Centro Hospitalar de Lisboa Ocidental,
Portugal
Case Report
DIPNECH (Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia): A Rare Syndrome or Undiagnosed?
Author(s): Rafaela B. Campanha, Cristina Matos and Fernando NogueiraRafaela B. Campanha, Cristina Matos and Fernando Nogueira
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH) is considered a rare syndrome and knowledge of its pathophysiology is scarce. Classified as pre-neoplastic lesion of carcinoid tumours currently there are many questions regarding the best approach to follow-up and treatment this patients. Mainly affects females, there is no apparent relationship to smoking habit and is often confused with obstructive airway disease. The diagnosis is histological and sometimes can be observed simultaneously a triple pattern consisting of DIPNECH, tumourlets and carcinoid tumour. We report the case of a 35-years-old woman, non-smoker with DIPNECH in association with typical carcinoid tumour and tumourlets.
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DOI:
10.4172/2161-105X.1000286
Pulmonary & Respiratory Medicine received 1690 citations as per Google Scholar report