Division of Critical Care Medicine, Tokyo Medical University Hachioji Medical Center, Hachioji, Tokyo, Japan
Case Report
A Case of Spinal and Bulbar Muscular Atrophy Requiring Amputation and Airway Support
Author(s): Haruka Makinae*, Taichiro Takamatsu, Akimasa Suzuki and Hidenobu Kamohara
Spinal and bulbar muscular atrophy (SBMA) is a rare neuromuscular disorder. Here, we present the case of a 53-year-old male diagnosed with
SBMA, who underwent left leg amputation for a compound fracture with gas gangrene. The patient was hospitalized with gas gangrene and sepsis,
and required non-invasive positive pressure ventilation, inotropes, and continuous hemodiafiltration. The patient gave consent for mechanical
ventilation and underwent an amputation. Before and after the amputation, the patient had recurrent severe atelectasis of the left lower lobe, and
large emboli composed of coagulated blood cells and sputum were extracted. SBMA itself is not curable, although the morbidity and complications
related to SBMA can be managed using essential procedures... Read More»
DOI:
10.37421/2165-7920.2023.13.1554
Journal of Clinical Case Reports received 1345 citations as per Google Scholar report