Department of Medicine, Smt. N.H.L. Municipal Medical College and SVPISMR, Ahmedabad, Gujarat, India
Case Reports
An Unusual Presentation of Thrombotic Thrombocytopenic Purpura with Preserved ADAMTS13: A Case Report
Author(s): Nyein Wint Yee Theik, Vedant Shah, Abhi Shah*, Viraj Panchal, Bhavya Vyas and Sanket Bharadwaj
Background: Thrombotic Thrombocytopenic Purpura (TTP) is a rare, potentially fatal disease with multisystem
involvement. ADAMTS13 assays are often used for supporting the diagnosis, here we present a rare case of TTP with normal
ADAMTS13 levels.
Case presentation: A 39-year-old female presents with syncopal episodes, blurred vision in both eyes during a patch
test, headaches, and tenderness over the abdomen, all against a backdrop of hypertensive emergency. She had a history of
chronic hypertension managed on medications, iron deficiency secondary to fibroid and an episode of provoked deep vein
thrombosis and pulmonary embolism with negative work-up of thrombophilia. Labs revealed low hemoglobin of 9.8 mg/dl, platelet in the
range of 52,000/ ml, 3 mEq/L potassium, with high levels of Creatinine (Cr) 6.7 mg/dl and Blood Urea N.. Read More»
DOI:
10.37421/ 2165-7831.2024.14.318
Journal of Blood & Lymph received 443 citations as per Google Scholar report